Abta-Letterter-Sieve disease
Abta-Letterter-Sieve disease
Abet-Letterer-Sieve disease - acute reticulosiswhich is a systemic malignant disease with a steadily progressing course. Reticulosis is a common name for diseases based on malignant systemic proliferation (change) of the reticular cells that make up the reticular stroma of the hematopoietic organs.
Instructions
1
This disease is noted in children up to 3-5 years. The initial signs of the disease are general weakness, pallor, loss of appetite, headache and fever, which persists for several weeks. The disease is accompanied by hypochromic anemia, enlarged lymph nodes and frequent lysis (destruction) of bones, especially the skull, pelvis, ribs, thighs. Radiographic examination reveals defects in bones, round or irregular in shape, of various sizes.
2
The defeat of the skin is the development of purpura(pigmentation) skin changes, occasionally ulcers of different sizes, bright pink or yellowish-brown spots, nodules on the skin. Eruptions are located primarily on the skin of the face, head or trunk. Very often people with this disease make an erroneous diagnosis - seborrheic eczema, tk. The signs of these two diseases are closely similar. Unlike eczema in the case of Abta-Letterter-Siva disease, necrosis followed later with the formation of scars in the center of the papules and nodules. Sometimes changes on the skin are accompanied by wetting and severe itching, serous and hemorrhagic crusts.
3
Treatment for diseasesAbta-Letterera-Siwe: blood transfusion, plasma, glucose, vitamins. Assign corticosteroid drugs in combination with antibiotics and radiation therapy. Taking glucocorticoids is especially necessary, as they depress the function of the reticulogistiocyte system, stimulate hemopoiesis, normalize the metabolism, etc. They are prescribed for a long time - until the disappearance of the clinical signs of the disease.
